POLAND’S SYNDROME

Poland's syndrome is a rare, non-genetic disorder characterized by:

1. Unilateral shortening of the digits (mainly the index, long and ring finger mainly due to a short or absent middle phalanx).
2. Syndactyly of the shortened digits (usually a simple complete type).
3. Hypoplasia of the hand, and to a lesser extent the forearm.
4. Absence of the sternocostal head of pectoralis major muscle on the same side associated to a decreasing degree with:
• Absent pectoralis minor muscle.
• Hypoplasia of the breast and nipple (33% of affected females).
• Contraction of the anterior axillary fold.
• Absence of serratus anterior, latissimus dorsi and deltoid.
• Rib deficiencies, thoracic scoliosis and dextrocardia.

Other anomalies associated with Poland's syndrome include Pierre Robin syndrome.