CLASSIFICATION OF OTOCEPHALY

Type I	Isolated agnathia
Type II	Agnathia with holoprosencephaly
Type III	Agnathia with situs inversus and visceral anomalies
Type IV	Agnathia, holoprosencephaly, situs inversus and other visceral anomalies

REFERENCES

1. Leech RW, Bowlby LS, Brumback RA et.al. Agnathia, holoprosencephaly, and situs inversus: Report of a case. Am J Med Genet 1988;29:483.