POTTER CLASSIFICATION OF CYSTIC RENAL DISEASE

 

 

Type 1

Infantile (autosomal recessive) polycystic disease of kidney.

Type II
 
IIA
IIB

Multicystic renal dysplasia.
Multilocular cystic nephroma.
Kidneys of normal / increased size.
Kidneys reduced in size.

Type III

Adult polycystic disease of the kidneys.
Tuberous sclerosis.
Medullary sponge kidney.

Type IV

Small cortical cysts / cystic renal dysplasia secondary to ureteropelvic junction obstruction.

 

 

 

REFERENCES

  1. Osathanondh V, Potter EL. Pathogenesis of polycystic kidneys. Arch Pathol 1964;77:459-512.